врождённая лучевая косорукость
English translation: congenital radial clubhand /Madelung's deformity /Talipomanus Manus vara
| 20:26 Oct 20, 2002 |
| Russian to English translations [PRO] Medical | |||||||
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|  Selected response from: Natalie Poland Local time: 18:07 | ||||||
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Answers
4 mins confidence: 
Madelung's Disease / Launois-Bensaude Syndrome Explanation: So it would appear... A case of Launois-Bensaude Syndrome (Madelung's disease) in a chronic alsoholic is presented and the typical features are discussed. This entity should be considered in patients who present with doughy, symmetrically distributed, adipose masses. -------------------------------------------------------------------------------- Figure 1 Launois- Bensaude Syndrome or Madelung' s Disease, is rare disorder of unknown etiology. It was first described in 1898 by Launois and Bensaude.[1] Since this report, about 200 cases have been published in the literature.[2] The disease is characterized by prominent, symmetrical masses on the neck, shoulders, arms and uppers parts of the trunk, composed of symmetrically arranged adipose tissue, which gives a pseudoathletic appearance. The characteristic masses are doughy on palpation which distinguishes them from truly hypertrophied muscles. When well developed, these masses render neck movement and breathing more difficult.[3] The disease begins between 35 and 50 years of age and develops over a period of months to years. Males are more often affected than females. The disease can be associated with hyperlipoproteinemia, hyperuricemia, diabetes mellitus and chronic alcoholism.[3] The only effective treatment is surgical removal or liposuction, but recurrences are common -------------------------------------------------- Note added at 2002-10-20 20:33:14 (GMT) -------------------------------------------------- AKA Benign Symmetric Lipomatosis or Multiple Symmetrical Lipomatosis (MSL) Benign Symmetric Lipomatosis Madelung\'s Disease Lanois-Bensaude Syndrome MSL, Multiple Symmetrical Lipomatosis, also known as Benign Symmetric Lipomatosis or Madelung\'s Disease and Lanois-Bensaude Syndrome is a metabolic condition characterized by the growth of fatty masses around the face, back of the head, neck, upper arms, abdomen, back and upper leg in a very specific pattern or distribution. Unlike the usual lipoma, these benign, fatty masses are not enclosed within a membranous capsule with very distinct boundaries. It is because of this characteristic, as well as the absolute symmetry in their occurrence that the condition is often dismissed as simple obesity. http://home.earthlink.net/~reilly65/MSL.html Reference: http://dermatology.cdlib.org/DOJvol7num2/case_presentations/... |
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